|
KMID : 0191120010160050683
|
|
Journal of Korean Medical Science
2001 Volume.16 No. 5 p.683 ~ p.688
|
|
|
Idiopathic Hypertrophic Spinal Pachymeningitis: A Case Report
|
|
Sung-Hye Park
C. Jin Whang/Moonjun Sohn/Yeun Chul Oh/Chae Hyuk Lee/Yoon Joon Whang
|
|
|
Abstract
|
|
|
Idiopathic hypertrophic pachymeningitis (IHP) is a rare, chronic nonspecific and granulomatous inflammatory
disorder of the dura with unknown etiology. The diagnosis can be established by open biopsy and exclusion
of all other specific granulomatous and infectious diseases. We report a typical case of spinal IHP
occurring in a long segment of cervical and thoracic dura from C6 to T8. The patient was 56-yr-old female,
who had been suffered from pain on her upper back and both arms for 3 months and recent onset motor weakness
of both legs. During the 9 months of follow-up period, she experienced the improvement of her neurologic
symptoms with combined therapy of partial excision and corticosteroid medication. Since early surgical
intervention and subsequent pulse steroid therapy are mandatory for this disease to avoid irreversible
damage of nervous system, the identification of this unique disease entity is essential on frozen diagnosis.
A few cases have been reported in Korean literature.
|
|
|
KEYWORD
|
|
|
|
|
|
FullTexts / Linksout information
|
|
 
|
|
|
Listed journal information
|
|
    
|